X-linked incontinentia pigmenti or Bloch-Sulzberger syndrome: a case report.

نویسندگان

  • Marcela A C Pereira
  • Lismary A de F Mesquita
  • Anelise R Budel
  • Carolina S P Cabral
  • Amanda de S Feltrim
چکیده

Incontinentia pigmenti is a rare X-linked genodermatosis that affects mainly female neonates. Skin manifestations are the most common and occur in four quite distinct phases. A female infant presented vesiculobullous lesions on trunk and limbs, and a verrucous lesion on the right palm. Biopsy revealed eosinophil exocytosis and pigment incontinence, confirming the clinical hypothesis. Although uncommon, incontinentia pigmenti should be taken into consideration as a possible differential diagnosis when vesiculobullous and verrucous lesions are present in childhood.

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Incontinenta pigmenti (Bloch-Sulzberger disease) در یک دختر 10 ساله

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عنوان ژورنال:
  • Anais brasileiros de dermatologia

دوره 85 3  شماره 

صفحات  -

تاریخ انتشار 2010